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Large focal nodular hyperplasia and extrahepatic portosystemic shunt in a male patient: Multi-modality imaging features


  • YX Kitzing MBBS; J Gallagher MBBS, FRACS; R Waugh MBBS, FRACR.

  • Conflict of interest: None.

Dr Yu Xuan Kitzing, Departments of Radiology, Royal Prince Alfred Hospital, Missenden Road, Camperdown, Sydney, NSW 2050, Australia. mail:


Congenital extrahepatic portocaval shunt is a rare condition that is described mostly in female patients. We report an unusual case of a young adult male patient with type 1 congenital extrahepatic portocaval shunt with associated development of a focal nodular hyperplasia on a background of regenerative nodules. With multi-slice CT utilisation, there is increased detection of portocaval malformation in asymptomatic patients. This congenital variant is clinically significant with associated development of hepatocellular lesions, hepatic dysfunction and/or encephalopathy.