Conflict of interest: The authors have no conflict of interest to disclose.
Retrospective cohort study of long-gap oesophageal atresia
Article first published online: 19 JUN 2013
© 2013 The Authors. Journal of Paediatrics and Child Health © 2013 Paediatrics and Child Health Division (Royal Australasian College of Physicians)
Journal of Paediatrics and Child Health
Volume 49, Issue 10, pages 845–849, October 2013
How to Cite
Maheshwari, R., Trivedi, A., Walker, K. and Holland, A. J. (2013), Retrospective cohort study of long-gap oesophageal atresia. Journal of Paediatrics and Child Health, 49: 845–849. doi: 10.1111/jpc.12299
- Issue published online: 17 OCT 2013
- Article first published online: 19 JUN 2013
- Manuscript Accepted: 22 MAR 2013
- growth and development;
- oesophageal atresia
Long-gap oesophageal atresia (LGOA) remains a rare variant of a relatively common congenital malformation. Objectives of this study were to review the short-term results including survival, length of stay and post-operative complications for infants with LGOA managed at a single centre in addition to their growth and neurodevelopmental assessment.
Retrospective review of the case notes of all infants admitted with oesophageal atresia to our institution from January 2001 to May 2011. Infants with LGOA were selected based on pre-defined criteria. Demographic and clinical variables and details of follow-up visits including developmental assessments were extracted from their case notes.
Of 101 infants with oesophageal atresia, 15 fulfilled the criteria for LGOA. Overall survival was 80%. Median length of stay was 83 days. Additional congenital anomalies were present in nine (60%). A fall in weight centile during hospitalisation or outpatient follow-up signifying growth failure was seen in a majority with 11 of 13 patients showing this phenomenon. Follow-up at our institution ranged from 6 months to 9 years. Developmental assessments (Bayley-III) commenced in August 2006 were available in four patients (age 5–13 months) and were abnormal in all, with particular delay in the gross motor domain.
Infants with LGOA spend a long time in hospital. They remain at significant risk of growth failure during hospitalisation and following discharge. There appears to be a risk of developmental delay that warrants close monitoring.