Financial disclosure: None reported.
Recurrent Facial Erythema with Burning Sensation and Increased Temperature: A Variant of Erythromelalgia or a New Entity?
Article first published online: 16 JAN 2014
Wiley Periodicals, Inc
Volume 15, Issue 6, pages 1007–1010, June 2014
How to Cite
Luo, D.-Q., Zhao, Y.-K., Xu, Q.-F., He, X.-Q. and Wu, L.-C. (2014), Recurrent Facial Erythema with Burning Sensation and Increased Temperature: A Variant of Erythromelalgia or a New Entity?. Pain Medicine, 15: 1007–1010. doi: 10.1111/pme.12343
Conflicts of interest: All authors have no conflicts of interest.
Prior presentation: None.
Funding sources: None.
- Issue published online: 26 JUN 2014
- Article first published online: 16 JAN 2014
Erythromelalgia is a rare clinical syndrome characterized by episodic attacks of burning pain, erythema, and increased temperature, primarily affecting the extremities, and in rare instances, involving the ear, face, neck, and the scrotum. The dermatoscopic features of erythromelalgia in a case with solely facial involvement have never been described previously.
We describe a 14-year-old female who presented with erythema, burning sensation, and warmth on her face only, which mimic the features of erythromelalgia. Physical examination showed higher temperature on the involved cheeks than on axillas during the episode, while the temperature on both areas was the same between episodes. Dermatoscope showed more dilated vessels inside the erythema during the episodes than between the episodes. The symptoms had excellent response to the combination treatment of gabapentin, indomethacin, and topical lidocaine compounds.
The present case is considered to be a variant of erythromelalgia. Its erythema may be resulted from the dilated vessels. Combination of modalities may provide effective management for erythromelalgia. “Erythermalgia” may be better than “erythromelalgia” to describe such conditions.