Isolated Supravalvular Pulmonary Stenosis: A Rare Echocardiographic Finding
Stefano Maffè, Pierfranco Dellavesa, Paola Paffoni, Franco Zenone, Lorenzo Cucchi, Anna Maria Paino, Luca Bergamasco, Lara Baduena, Nicolò Franchetti Pardo, Marco Zanetta and Umberto Parravicini
Article first published online: 5 APR 2014 | DOI: 10.1111/echo.12612
Here, we report a case of a 76-year-old patient with isolated, severely obstructive, pulmonary supravalvular stenosis. The peculiarity of the present case is the paucity of symptoms and lack of changes in right heart sections, despite of the importance of stenosis. The report confirms the utility of transthoracic two- and three-dimensional echocardiography and transesophageal echocardiography in the detection and quantification of this rare anomaly.